52 -7 (45) 2022 — Furkat A. Otamuradov, Nasriddin Sh. Ergashev — RARE REGIONAL FORMS OF ANORECTAL MALFORMATION IN CHILDREN

RARE REGIONAL FORMS OF ANORECTAL MALFORMATION IN CHILDREN

Furkat A. Otamuradov, Termez branch of the Tashkent Medical Academy, Termez, Uzbekistan

Nasriddin Sh. Ergashev Tashkent Pediatric Medical Institute, Tashkent, Uzbekistan

Resume

The article presents literature data and own observations of 121 children with rare regional variants of anorectal malformations. The indicated forms accounted for 24.1% in the general structure of AWP with fluctuations from 0.83% to 24% among various nosological forms; prevailed among girls – 95 (78.5%), among boys – 26 (21.5%). Ectopia of the anus was observed in 25.6% of cases; H-form rectogenital fistulas with a normally formed anus in 24%; atresia with rectovaginal fistula in 18.2%. Cases of rectal duplication, exstrophy of the cloaca, and urogenital fistula are presented. The nature and frequency of concomitant pathology in various nosological forms have been analyzed.

Key words: anorectal malformations, rare regional variants, diagnosis.

First page

263

Last page

272

For citation: Furkat A. Otamuradov, Nasriddin Sh. Ergashev RARE REGIONAL FORMS OF ANORECTAL MALFORMATION IN CHILDREN //New Day n Medicine 7(45)2022 263-272 https://clck.ru/sKyJG

LIST OF REFERENCES:

1. Аверин В.И., Ионов А.Л., Караваева С.А., Комисаров И.А., Котин А.Н., Мокрушина О.Г., Морозов Д.А., и др. Аноректальные мальформации у детей (Федеральные клинические рекомендации) // Детская хирургия. – Москва, 2015. – № 4. – С. 29-35.
2. Крушельницкая Ю.В. Эпидемиологическая и клинико-генетическая характеристика врожденных пороков развития желудочно-кишечного тракта у детей. /Автореферат дисс. к.м.н., Москва 2018г. 24С.
3. Морозов Д.А., Окулов Е.А., Пименова Е.С. Российский консенсус по хирургическому лечению детей с аноректальными пороками. Первые шаги // Российский вестник детской хирургии, анестезиологии и реаниматологии. – Москва, 2013. – №4. – С.8-13.
4. Эргашев Н.Ш., Отамурадов Ф.А. Редкие региональные формы аноректальных мальформаций у девочек. Диагностика и тактика лечение. // Российский вестник детской хирургии, анестезиологии и реаниматологии. – Москва, 2016. – № 3. – С. 40-44.
5. Endo M, Hayashi A, Ishihana M, et al (1999) Analysis of 1992 patients with anorectal malformations over the past 2 decades in Japan. // J Pediatr Surg 34:435-441
6. Holschneider A., Hutson J., Pena A., Bekhit E., Chatterjee S., Coran A. et al.  Preliminary report on the International Conference for the Development of Standards for the Treatment of Anorectal Malformations // Journal of Pediatric Surgery. – (USA), 2005. – Vol. 40 N 5. – pp. 1521-1526.
7. Holschneider A., Hutson J. Anorectal Malformations in Children. Embryology, diagnosis, surgical treatment, follow-up. – // Heidelberg: Springer, 2006. P 251
8. I.de BLaauw, Wijers C.H.W., Schnriedeke E., Holland-Cunz S., Gamba P., Marcelis C.L.M., Reutter H., Aminoff D., Schipper M., Schwarzer N., Grasshoff-Derr S., Midrio P., Jenetzky E., van Rooij I.A.L.M. First results of a European multi-center registry of patients with anorectal malformations // Journal of Pediatric Surgery. – (USA), 2013. – Vol.48, № 12. – pp. 2530-2535.
9. Lawal T.A., Chatoorgoon K., Bischoff A., Pena A., Levvit M.A. Manegment of H-type rectovestibular and rectovaginal fistulas. // J Pediatr Surg. 2011; 46(6):1226-1230.
10. Levitt M.A., Pena A. В кн.: Ashcraft’s Pediatric Surgery 6th Edition. George W. Holcomb III. 2014, 492 стр
11. Pena A, Levitt M: Anorectal malformations . In Pediatric Surgery and Urology: Long term outcomes 2nd edition. Edited by: Stringer M,Oldham K, Mouriquand PDE. // Cambridge: Cambridge University Press; 2006: р. 401-415.