7 -4 (66) 2024 - Madiev R.Z., Berdiev E.A. - THE FIRST CASE OF SURGICAL CORRECTION OF HIGH PULMONARY HYPERTENSION WITH A MATHEMATICAL APPROACH IN A CHILD WITH A RARE VARIANT OF RARE CONGENITAL HEART DEVICE

THE FIRST CASE OF SURGICAL CORRECTION OF HIGH PULMONARY HYPERTENSION WITH A MATHEMATICAL APPROACH IN A CHILD WITH A RARE VARIANT OF RARE CONGENITAL HEART DEVICE

Madiev R.Z. Termez branch of the TashkentMedical Academy, Surkhandarya region

Berdiev E.A. Tashkent Medical Academy (TMA) Uzbekistan

Barskaya L.I. Termez branch of the TashkentMedical Academy, Surkhandarya region

Resume

Truncus arteriosus (TA) is a rare congenital heart defect. In this case, from the base of the heart - from both ventricles, one common great vessel (TA) departs, which has one valve ring, consisting of two to six semilunar valves. The pulmonary artery (PA) or its branches arise from the ascending part of the TA - above its valve ring and to the level of the beginning of the brachiocephalic arteries. Underneath the TA there is a large crescent-shaped ventricular septal defect. From both ventricles there is a pathological release of blood through the ventricular septal defect into the TA with mixing of blood in it. TA provides coronary, systemic and pulmonary circulation. The worldwide accepted classification of TA according to R. Collett and J. Edwards (1949) divides this defect into 4 types. The detection rate of TA among congenital heart defects ranges from 0.2 – 1.0% to 1.7%. Among them, the most common type is type I. In this case, the LA departs from the TA and divides into two branches. In type II, the PA branches extend from the posterior wall of the TA, and their openings are located next to each other. Type II TA has 2 anatomical directions: a – without PA stenosis, b – with PA stenosis. A feature of TA type IIa is the rapid malignant development of high pulmonary hypertension (HPH) and Eisenmenger syndrome with a low chance of reaching age without surgery. The world literature mainly describes surgical correction of type I TA. However, there are no reports on the incidence and surgical treatment of TA type IIa. Using the example of a single case in cardiac surgical practice of surgical correction of TA type II a, complicated by 100% HPH in a sick infant, the effectiveness of narrowing of both branches of the pulmonary artery was demonstrated using a mathematical approach according to the technique of cardiac surgeon R.Z. Madieva.

Keywords: Truncus arteriosus (TA), pulmonary artery (PA), high pulmonary hypertension (HPH), type IIa TA, narrowing of the branches of the PA in children according to the method of cardiac surgeon R.Z. Madieva, mathematical approach.

First page

40

Last page

47

For citation: Madiev R.Z., Berdiev E.A., Barskaya L.I. - THE FIRST CASE OF SURGICAL CORRECTION OF HIGH PULMONARY HYPERTENSION WITH A MATHEMATICAL APPROACH IN A CHILD WITH A RARE VARIANT OF RARE CONGENITAL HEART DEVICE//New Day in Medicine 4(66)2024 40-47 https://newdayworldmedicine.com/en/article/3758

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